Clinical Illustration: Autosomal Recessive Polycystic Kidney Disease

This article presents illustrative images suggestive of autosomal recessive polycystic kidney disease (ARPKD) from a young child born at full-term gestational age.She had a prior history of repeated episodes of fevers, and during her systemic evaluation, she was noted to have abnormal plasma renal function indices.Renal ultrasound showed enlarged kidneys with increased echogenicity, multiple cysts of varying sizes, and loss of normal corticomedullary differentiation.Sonographic images of the liver showed two anechoic cystic areas, possibly representing a combination of von Meyenburg complexes (biliary hamartomas) and focal intrahepatic biliary dilation, indicating Caroli disease.