Mortality rates in adults with severe congenital heart disease: insights from the National Congenital Heart Disease Registry of Australia

Adults with severe lesions, particularly single-ventricle physiology, remain at high risk of premature mortality. Patients managed in Sydney/Melbourne had better survival, possibly reflecting the influence of long-established specialist ACHD programs, although residual confounding cannot be excluded. Urban-rural outcome parity suggests that Australia's centralised care model mitigates geographical barriers.

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Publication Details

Journal
International Journal of Cardiology Congenital Heart Disease
Published
2025-10-18
DOI
https://doi.org/10.1016/j.ijcchd.2025.100629
Primary Topic
Congenital Heart Disease Studies
Type
article
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0.00
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article

Mortality rates in adults with severe congenital heart disease: insights from the National Congenital Heart Disease Registry of Australia

Rachael Cordina, David S. Celermajer, Calum Nicholson, Geoff Strange et al.
International Journal of Cardiology Congenital Heart Disease
Congenital Heart Disease Studies
article

Mortality rates in adults with severe congenital heart disease: insights from the National Congenital Heart Disease Registry of Australia

Rachael Cordina, David S. Celermajer, Calum Nicholson, Geoff Strange, Jason Chami, David W. Baker
article en

Abstract

Adults with severe lesions, particularly single-ventricle physiology, remain at high risk of premature mortality. Patients managed in Sydney/Melbourne had better survival, possibly reflecting the influence of long-established specialist ACHD programs, although residual confounding cannot be excluded. Urban-rural outcome parity suggests that Australia's centralised care model mitigates geographical barriers.

International Journal of Cardiology Congenital Heart DiseaseVol. 22
The University of Sydney (AU), Royal Prince Alfred Hospital (AU), The Heart Research Institute (AU), The University of Notre Dame Australia (AU)
Openalex Percentile: Top 60%
Congenital Heart Disease Studies
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Mortality rates in adults with severe congenital heart disease: insights from the National Congenital Heart Disease Registry of Australia — Rachael Cordina, David S. Celermajer, et al. · International Journal of Cardiology Congenital Heart Disease (2025) | TGRS Research Map | TGRS