Bilateral Sudden on Chronic Hearing Loss as an Auditory Manifestation of Mitochondrial <scp>DNA</scp> Mutations
We presented a series of patients with a mitochondrial DNA mutation who presented to our clinic with sudden bilateral sudden on chronic sensorineural hearing loss; these patients responded well to cochlear implantation. In cases of sudden sensorineural hearing loss-particularly when clinical features raise suspicion for an underlying mitochondrial disorder-genetic testing may offer valuable diagnostic insight and assist in guiding appropriate management strategies.
Authors
- Chen‐Chi Wu (ORCID: https://orcid.org/0000-0002-5047-2204)
- Cheng‐Yu Tsai (ORCID: https://orcid.org/0000-0001-6150-4577)
- Li‐Hui Tseng (ORCID: https://orcid.org/0000-0002-8308-6772)
- Ni‐Chung Lee (ORCID: https://orcid.org/0000-0002-5011-7499)
- Chun‐Kang Liao (ORCID: https://orcid.org/0000-0002-0037-1421)
- C.-C. Liu (ORCID: https://orcid.org/0000-0003-2580-2942)
- Pei‐Hsuan Lin (ORCID: https://orcid.org/0000-0001-5028-8434)
- Yan Han-min
Institutions
- National Taiwan University Hospital (TW)
- National Yunlin University of Science and Technology (TW)
Publication Details
- Journal
- The Laryngoscope
- Published
- 2025-10-17
- DOI
- https://doi.org/10.1002/lary.70208
- Citations
- 2
- Primary Topic
- Mitochondrial Function and Pathology
- Type
- article
- Field-Weighted Citation Impact
- 1.61