Clinical Spectrum, Pathology, and Mechanisms of Anti-LGI4 Antibody–Positive Autoimmune Nodopathy
LGI4<sup>+</sup> AN manifests as acute/subacute monophasic and chronic progressive/relapsing diseases, sometimes exhibiting nerve hypertrophy with onion bulbs through nonmyelinating Schwann cell proliferation.
Authors
- Noriko Isobe (ORCID: https://orcid.org/0000-0001-9525-4254)
- Ryota Sato (ORCID: https://orcid.org/0000-0003-1691-1776)
- Masaki Fukata (ORCID: https://orcid.org/0000-0001-5200-9806)
- Tomohiro Imamura (ORCID: https://orcid.org/0000-0003-2277-9134)
- Yoshio Tsuboi (ORCID: https://orcid.org/0000-0002-6758-0981)
- Jun‐ichi Kira (ORCID: https://orcid.org/0000-0001-5307-2671)
- Akira Yokote (ORCID: https://orcid.org/0000-0003-2645-2964)
- Ayako Sakoda (ORCID: https://orcid.org/0000-0003-2334-428X)
- Mikio Mitsuishi
- Hidenori Ogata (ORCID: https://orcid.org/0000-0001-8932-9731)
- Toshihiro Ide (ORCID: https://orcid.org/0000-0002-3458-7159)
- Takayasu Mishima (ORCID: https://orcid.org/0000-0002-4649-0434)
- Yuko Fukata (ORCID: https://orcid.org/0000-0001-7724-8643)
- Haruki Koike (ORCID: https://orcid.org/0000-0002-4612-3183)
- Kazuo Kitagawa (ORCID: https://orcid.org/0000-0002-7669-231X)
- Guzailiayi Maimaitijiang (ORCID: https://orcid.org/0000-0003-3285-2462)
- Takumi Tashiro
- Xu Zhang (ORCID: https://orcid.org/0000-0002-9817-4492)
- Masaki Kobayashi (ORCID: https://orcid.org/0000-0003-2738-9792)
- Takashi Kanda (ORCID: https://orcid.org/0000-0001-8919-6377)
- Yusuke Ohya (ORCID: https://orcid.org/0000-0001-7709-5640)
- Kenichiro Yamashita (ORCID: https://orcid.org/0000-0002-1409-6504)
- Yukihiro Namihira (ORCID: https://orcid.org/0000-0003-2121-2232)
- Yuri Nakamura
Institutions
- Kyushu University (JP)
- Yamaguchi University (JP)
- Saga University (JP)
- National Kyushu Medical Center (JP)
- Fukuoka University (JP)
- University of the Ryukyus (JP)
- Fukuoka International University (JP)
- Tokyo Women's Medical University Hospital (JP)
- Shimonoseki City Hospital (JP)
- Nagoya University (JP)
- International University of Health and Welfare (JP)
Publication Details
- Journal
- Neurology Neuroimmunology & Neuroinflammation
- Published
- 2025-10-15
- DOI
- https://doi.org/10.1212/nxi.0000000000200504
- Primary Topic
- Peripheral Neuropathies and Disorders
- Type
- article
- Field-Weighted Citation Impact
- 0.00