Clinical Spectrum, Pathology, and Mechanisms of Anti-LGI4 Antibody–Positive Autoimmune Nodopathy

LGI4<sup>+</sup> AN manifests as acute/subacute monophasic and chronic progressive/relapsing diseases, sometimes exhibiting nerve hypertrophy with onion bulbs through nonmyelinating Schwann cell proliferation.

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Publication Details

Journal
Neurology Neuroimmunology & Neuroinflammation
Published
2025-10-15
DOI
https://doi.org/10.1212/nxi.0000000000200504
Primary Topic
Peripheral Neuropathies and Disorders
Type
article
Field-Weighted Citation Impact
0.00
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article

Clinical Spectrum, Pathology, and Mechanisms of Anti-LGI4 Antibody–Positive Autoimmune Nodopathy

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Neurology Neuroimmunology & Neuroinflammation
Peripheral Neuropathies and Disorders
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Clinical Spectrum, Pathology, and Mechanisms of Anti-LGI4 Antibody–Positive Autoimmune Nodopathy

Noriko Isobe, Ryota Sato, Masaki Fukata, Tomohiro Imamura, Yoshio Tsuboi, Jun‐ichi Kira, Akira Yokote, Ayako Sakoda, Mikio Mitsuishi, Hidenori Ogata, Toshihiro Ide, Takayasu Mishima, Yuko Fukata, Haruki Koike, Kazuo Kitagawa, Guzailiayi Maimaitijiang, Takumi Tashiro, Xu Zhang, Masaki Kobayashi, Takashi Kanda, Yusuke Ohya, Kenichiro Yamashita, Yukihiro Namihira, Yuri Nakamura
article en

Abstract

LGI4<sup>+</sup> AN manifests as acute/subacute monophasic and chronic progressive/relapsing diseases, sometimes exhibiting nerve hypertrophy with onion bulbs through nonmyelinating Schwann cell proliferation.

Neurology Neuroimmunology & NeuroinflammationVol. 12(6)
Kyushu University (JP), Yamaguchi University (JP), Saga University (JP), National Kyushu Medical Center (JP), Fukuoka University (JP), University of the Ryukyus (JP), Fukuoka International University (JP), Tokyo Women's Medical University Hospital (JP), Shimonoseki City Hospital (JP), Nagoya University (JP), International University of Health and Welfare (JP)
Openalex Percentile: Top 58%
Peripheral Neuropathies and Disorders
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