Case Report: Spontaneous pneumomediastinum in a patient with MDA5-positive dermatomyositis and severe pulmonary fibrosis

This case emphasizes the complexity of managing anti-MDA5-positive DM with severe pulmonary complications. Early recognition, a multidisciplinary approach, and personalized treatment are crucial to improving outcomes.

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Publication Details

Journal
Frontiers in Medicine
Published
2025-10-13
DOI
https://doi.org/10.3389/fmed.2025.1646791
Primary Topic
Inflammatory Myopathies and Dermatomyositis
Type
article
Field-Weighted Citation Impact
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article

Case Report: Spontaneous pneumomediastinum in a patient with MDA5-positive dermatomyositis and severe pulmonary fibrosis

Andrea Lo Monaco, C R Braga, Beatrice Maranini, Gioacchino Schifino et al.
Frontiers in Medicine
Inflammatory Myopathies and Dermatomyositis
article

Case Report: Spontaneous pneumomediastinum in a patient with MDA5-positive dermatomyositis and severe pulmonary fibrosis

Andrea Lo Monaco, C R Braga, Beatrice Maranini, Gioacchino Schifino, M. Govoni, Aldo Carnevale, M C Rizzo, M. Raschellà
article en

Abstract

This case emphasizes the complexity of managing anti-MDA5-positive DM with severe pulmonary complications. Early recognition, a multidisciplinary approach, and personalized treatment are crucial to improving outcomes.

Frontiers in MedicineVol. 12
University of Ferrara (IT), Arcispedale Sant'Anna (IT)
Openalex Percentile: Top 61%
Inflammatory Myopathies and Dermatomyositis
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