Unilateral pulmonary artery atresia: Imaging findings with diagnostic considerations

Unilateral pulmonary artery atresia is a rare condition requiring high index of suspicion for diagnosis. It occurs more frequently on the right side which is usually isolated in contrast to the left sided pulmonary atresia which is commonly associated with other congenital cardiac abnormalities and right aortic arch. Multimodal imaging is often required to make an accurate early diagnosis. Timely management is crucial for preventing complications and improving patient outcomes.