Characteristics, treatment and lung function outcomes of pulmonary exacerbations in cystic fibrosis: insights from the BEAT-CF cohort
The pattern and magnitude of lung function impairment during PERITs is similar among those receiving and not receiving modulator therapy. This underscores the continued need for evidence to help clinicians balance treatment burden against the risk of irreversible loss of lung function.
Authors
- Ameneh Khatami (ORCID: https://orcid.org/0000-0001-9114-6694)
- Lucy Burr (ORCID: https://orcid.org/0000-0003-4010-3787)
- Tom Snelling (ORCID: https://orcid.org/0000-0003-4670-0638)
- Hiran Selvadurai
- Edward Pan (ORCID: https://orcid.org/0000-0002-2676-1639)
- Geshani Jayasuriya
- Sheila Sivam (ORCID: https://orcid.org/0000-0002-7024-5543)
- Parveen Fathima (ORCID: https://orcid.org/0000-0002-4516-4127)
- Adam Jaffé (ORCID: https://orcid.org/0000-0002-1963-5415)
- André Schultz (ORCID: https://orcid.org/0000-0002-2000-8910)
- Julie Marsh (ORCID: https://orcid.org/0000-0001-8984-6907)
- Shivanthan Shanthikumar (ORCID: https://orcid.org/0000-0001-6000-3180)
- Andrew Tai (ORCID: https://orcid.org/0000-0001-9240-5416)
- Richard Norman (ORCID: https://orcid.org/0000-0002-3112-3893)
Institutions
- The University of Sydney (AU)
- Mater Health Services (AU)
- Royal Children's Hospital (AU)
- The University of Queensland (AU)
- The University of Melbourne (AU)
- The Kids Research Institute Australia (AU)
- The University of Western Australia (AU)
- Curtin University (AU)
- Royal Prince Alfred Hospital (AU)
- Princess Margaret Hospital for Children (AU)
- Women's and Children's Hospital (AU)
- Taronga Conservation Society Australia (AU)
- Sir Charles Gairdner Hospital (AU)
- Children's Hospital at Westmead (AU)
- UNSW Sydney (AU)
- Mater Research (AU)
- Migration Institute of Australia (AU)
- Sydney Children's Hospital (AU)
- John Hunter Children's Hospital (AU)
- Institute for Respiratory Health (AU)
- Sydney Orthopaedic Research Institute (AU)
- Perth Children's Hospital
- The University of Adelaide (AU)
- Neuroscience Research Australia (AU)
Publication Details
- Journal
- European Respiratory Journal
- Published
- 2025-10-09
- DOI
- https://doi.org/10.1183/13993003.01349-2025
- Citations
- 2
- Primary Topic
- Cystic Fibrosis Research Advances
- Type
- article
- Field-Weighted Citation Impact
- 3.04