High glucocorticoid dependency and limited therapeutic response in Japanese patients with VEXAS syndrome: a multicentre retrospective study
This study highlights the difficulty of treating patients with VEXAS syndrome in Japan. The development of more effective treatments is urgently needed to reduce glucocorticoid dependence and improve patient outcomes.
Authors
- Yohei Kirino (ORCID: https://orcid.org/0000-0002-9488-661X)
- Satoshi Kobayashi (ORCID: https://orcid.org/0000-0002-7760-0771)
- Ryo Rokutanda (ORCID: https://orcid.org/0000-0001-5966-6403)
- Nobuhiro Oda (ORCID: https://orcid.org/0000-0003-3967-6414)
- Yuichiro Fujieda (ORCID: https://orcid.org/0000-0003-4705-341X)
- Hideaki Nakajima (ORCID: https://orcid.org/0000-0002-8967-4954)
- Mitsumasa Kishimoto (ORCID: https://orcid.org/0000-0002-4007-1589)
- Ken Nagahata (ORCID: https://orcid.org/0000-0002-5233-8308)
- Kaoru Takase‐Minegishi (ORCID: https://orcid.org/0000-0002-0025-2617)
- Toshimasa Shimizu (ORCID: https://orcid.org/0000-0003-0036-2039)
- Hiroaki Ida (ORCID: https://orcid.org/0000-0003-0295-0301)
- Kosuke Katsuo (ORCID: https://orcid.org/0000-0001-9585-5885)
- Nobuyuki Horita (ORCID: https://orcid.org/0000-0002-8200-0340)
- Kaori Uchino (ORCID: https://orcid.org/0000-0003-2983-2129)
- Noriyuki Takahashi (ORCID: https://orcid.org/0000-0003-1982-7019)
- Naoki Umeda
- Hiroyuki Hagiyama (ORCID: https://orcid.org/0009-0002-2481-1169)
- Hiroshi Fujiwara
- Naomi Tsuchida (ORCID: https://orcid.org/0000-0001-7203-884X)
- Yuji Miyoshi (ORCID: https://orcid.org/0000-0001-8724-6393)
- Hidenori Ohnishi (ORCID: https://orcid.org/0000-0002-2890-0305)
- Kaori KASHINO
- Yusuke Yoshida (ORCID: https://orcid.org/0000-0002-0774-0509)
- Naomichi Matsumoto (ORCID: https://orcid.org/0000-0001-9846-6500)
- Hiroshi Kobayashi (ORCID: https://orcid.org/0000-0002-0748-3784)
- Yuri Uchiyama (ORCID: https://orcid.org/0000-0002-4540-5277)
- Tomoyuki Asano
- Hiroyuki Yamaguchi (ORCID: https://orcid.org/0000-0001-9835-8040)
- Ayaka Maeda (ORCID: https://orcid.org/0000-0002-1102-0475)
- Daisuke Kobayashi (ORCID: https://orcid.org/0000-0002-0384-8678)
- Ichiro Mori (ORCID: https://orcid.org/0000-0001-5237-2445)
- Ayaka Kato (ORCID: https://orcid.org/0009-0009-2148-8475)
- Yoichi Takeuchi (ORCID: https://orcid.org/0000-0001-7031-0651)
- Yuji Ito (ORCID: https://orcid.org/0000-0001-6948-0338)
- Keiichi Akasaka
- Yukiko Hidaka
Institutions
- Kurume University (JP)
- Fukushima Medical University (JP)
- Sapporo Medical University (JP)
- Aichi Medical University (JP)
- Gunma University (JP)
- Kyorin University (JP)
- Kagawa University (JP)
- Hokkaido University (JP)
- Kyoto University (JP)
- Osaka Prefectural Medical Center (JP)
- Kurashiki Central Hospital (JP)
- Nagoya University Hospital (JP)
- Tokyo Medical University Hachioji Medical Center (JP)
- Osaka City General Hospital (JP)
- Yokohama City University Hospital (JP)
- Hiroshima General Hospital (JP)
- National Center of Neurology and Psychiatry (JP)
- Gifu University Hospital (JP)
- Kameda Medical Center (JP)
- Higashi Osaka City General Hospital (JP)
- Nagano Municipal Hospital (JP)
- Niigata University Medical and Dental Hospital (JP)
- Hiroshima University Hospital (JP)
- Teikyo University Chiba Medical Center (JP)
- Immune Regulation (United Kingdom) (GB)
- Yokohama Municipal Minato Red Cross Hospital (JP)
- Saitama Red Cross Hospital (JP)
- Tokyo Metropolitan Tama Medical Center (JP)
- Shiga Medical Center (JP)
- Onomichi General Hospital (JP)
- Gifu University (JP)
- Nagasaki University (JP)
- Onomichi City University (JP)
- Nagoya University (JP)
- Niigata University (JP)
- Yokohama City University (JP)
Publication Details
- Journal
- Modern Rheumatology
- Published
- 2025-10-09
- DOI
- https://doi.org/10.1093/mr/roaf095
- Citations
- 1
- Primary Topic
- Otitis Media and Relapsing Polychondritis
- Type
- article
- Field-Weighted Citation Impact
- 1.67