Validation of the 2019 EULAR/ACR classification criteria and clinical characteristics of childhood-onset Japanese patients with systemic lupus erythematosus
Although the EULAR/ACR-2019 criteria are generally applicable, the limited specificity for MCTD necessitates careful differential diagnosis. Japanese cSLE is commonly characterized by renal involvement, hypocomplementemia, and SLE-related autoantibody positivity.
Authors
- Hidehiko Narazaki (ORCID: https://orcid.org/0000-0002-7182-3800)
- Ryuhei Yasuoka
- Kunio Hashimoto
- Hitoshi Irabu (ORCID: https://orcid.org/0000-0003-4370-4975)
- Masaki Shimizu (ORCID: https://orcid.org/0000-0003-1077-7772)
- Yuichi Yamasaki (ORCID: https://orcid.org/0000-0003-1765-1494)
- Shiro Ohshima (ORCID: https://orcid.org/0000-0003-1607-3979)
- Yasuo Nakagishi
- Masaaki Mori (ORCID: https://orcid.org/0000-0003-2130-4866)
- Miwa Goto (ORCID: https://orcid.org/0000-0002-4404-8159)
- Tomo Nozawa (ORCID: https://orcid.org/0000-0002-7072-0463)
- Akihiro Nakamura (ORCID: https://orcid.org/0000-0001-7349-5102)
- Hiroyuki Ishida (ORCID: https://orcid.org/0000-0002-6570-3757)
- Asami Ohara
- Hiroaki Umebayashi
- Daisuke Fukuhara (ORCID: https://orcid.org/0000-0003-1932-4841)
- Susumu Nishiyama (ORCID: https://orcid.org/0000-0003-0071-3011)
- Naomi Iwata
- Yuko Hayashi (ORCID: https://orcid.org/0000-0002-3195-3213)
- Takako Miyamae
Institutions
- Tokyo Medical and Dental University (JP)
- St. Marianna University School of Medicine (JP)
- Aichi Medical University (JP)
- Kyorin University (JP)
- Hamamatsu University School of Medicine (JP)
- Miyagi Children's Hospital (JP)
- Kyoto City Hospital (JP)
- Kurashiki Medical Center (JP)
- Life Science Institute (JP)
- Children's Medical Center (IR)
- Kagoshima University Hospital (JP)
- Osaka Minami Medical Center (JP)
- Kobe Children's Hospital (JP)
- Tokyo Women's Medical University (JP)
- Nagasaki University (JP)
- University of Yamanashi (JP)
- Nippon Medical School (JP)
- Yokohama City University (JP)
Publication Details
- Journal
- Modern Rheumatology
- Published
- 2025-10-07
- DOI
- https://doi.org/10.1093/mr/roaf088
- Primary Topic
- Systemic Lupus Erythematosus Research
- Type
- article
- Field-Weighted Citation Impact
- 0.00