Total anomalous pulmonary venous connection: mixed variation [2(1/2) + 1(1/2)] type: Bizarre Pattern: a case report

Among all variants of total anomalous pulmonary venous connection, mixed variety is a rare congenital anomaly. It comprises 3 different patterns including 2+2, 3+1, bizarre variations. These bizarre variations are uncommon findings in mixed variety. In this particular case, we report surgical correction of such rare variation comprising [2(1/2) cardiac + 1(1/2) supracardiac] type of pulmonary venous drainage. These variations impose the importance of preoperative delineation of heterogeneous venous drainage and subsequent planning for surgical repair.

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Publication Details

Journal
Journal of Cardiology & Cardiovascular Surgery
Published
2025-09-27
DOI
https://doi.org/10.51271/jccvs-0061
Primary Topic
Congenital Heart Disease Studies
Type
article
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article

Total anomalous pulmonary venous connection: mixed variation [2(1/2) + 1(1/2)] type: Bizarre Pattern: a case report

Reha Kakkar, Manpal Loona, Neeraj Kumar, Preeti Gusian
Journal of Cardiology & Cardiovascular Surgery
Congenital Heart Disease Studies
article

Total anomalous pulmonary venous connection: mixed variation [2(1/2) + 1(1/2)] type: Bizarre Pattern: a case report

Reha Kakkar, Manpal Loona, Neeraj Kumar, Preeti Gusian
article en

Abstract

Among all variants of total anomalous pulmonary venous connection, mixed variety is a rare congenital anomaly. It comprises 3 different patterns including 2+2, 3+1, bizarre variations. These bizarre variations are uncommon findings in mixed variety. In this particular case, we report surgical correction of such rare variation comprising [2(1/2) cardiac + 1(1/2) supracardiac] type of pulmonary venous drainage. These variations impose the importance of preoperative delineation of heterogeneous venous drainage and subsequent planning for surgical repair.

Journal of Cardiology & Cardiovascular SurgeryVol. 3(3)
Openalex Percentile: Top 63%
Congenital Heart Disease Studies
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