From infectious disease specialist to rheumatologist — difficulties in diagnosing autoinflammatory diseases using adult-onset Still’s disease an example

The article discusses the signs and diagnostic algorithm of autoinflammatory diseases, principles of therapy. Clinical manifestations and complications of adult-onset Still’s disease are discussed. The most serious complication of this pathology is macrophage activation syndrome. The data of the European clinical guidelines on the principles of treatment of adult-onset Still’s disease and drugs recommended for administration to patients with macrophage activation syndrome are presented. A clinical case of diagnosis of adult-onset Still’s disease in a 36-year-old woman is presented.