Kartagener's Syndrome With Complications: Diagnostic Challenges in a Resource‐Limited Setting
Kartagener's Syndrome (KS) is a rare genetic disorder characterized by bronchiectasis, chronic sinusitis, and situs inversus. This case report presents a 14-year-old girl from rural Bangladesh diagnosed with KS, who exhibited progressive respiratory distress, recurrent sinus infections, and primary amenorrhea. Diagnostic imaging revealed dextrocardia, bronchiectasis, and pulmonary hypertension. The patient was managed with oxygen therapy, chest physiotherapy, antibiotics, bronchodilators, diuretics, and hormonal support. This case highlights the challenges of diagnosing KS in low-resource settings and emphasizes the importance of early diagnosis and multidisciplinary care to prevent disease progression and improve patient outcomes.
Authors
- Nahid Afsar (ORCID: https://orcid.org/0009-0005-2219-2845)
- Asif Hasan (ORCID: https://orcid.org/0000-0002-5971-2550)
- A. K. M. Zahin
- Md. Habib‐E‐Rasul
- Md. Alfanuzzaman
Institutions
- Begum Rokeya University (BD)
Publication Details
- Journal
- Clinical Case Reports
- Published
- 2025-09-29
- DOI
- https://doi.org/10.1002/ccr3.71064
- Primary Topic
- Cystic Fibrosis Research Advances
- Type
- article
- Field-Weighted Citation Impact
- 0.00