Perivascular Cell Tumors (PEComas) of the Genitourinary Tract: A Summary

Perivascular cell tumors (PEComas) in the genitourinary tract have an overwhelming propensity to occur in the kidney, where they are synonymously referred to as angiomyolipomas (AMLs). Although less common, PEComas may occur throughout the urinary tract (particularly involving the bladder) and may rarely appear in the prostate/seminal vesicle and testis. Herein, we describe the wide clinicopathologic characteristics of genitorurinary PEComas both of renal and extrarenal origin.