An atypical case-spindle cell variant of embryonal rhabdomyosarcoma of mandible

Rhabdomyosarcoma (RMS) is an aggressive malignancy and commonest malignant soft tissue Sarcoma predominantly seen in children and young adults. This study presents a case of a spindle cell embryonal type RMS involving the mandible of a 17-year-young male with a localized disease who underwent a R0 resection with tumor free margins followed by adjuvant chemotherapy, now with recurrence and metastatic disease, currently on palliative therapy. This report emphasizes the significance of early diagnosis and accurate immunohistochemical analysis in achieving successful treatment outcomes for RMS.