Morgagnian cataract with congenital complete aniridia with congenital lenticular coloboma: A rare association

Complete congenital aniridia is a rare genetic ocular disease. We report a rare case of bilateral congenital complete aniridia in a 31-year-old male. He reported to the ophthalmology department when he experienced a significant decrease in vision in the right eye. On ocular examination, there was congenital complete aniridia with Morgagnian cataract with a congenital lenticular coloboma inferiorly in the right eye. The left eye also showed the presence of complete aniridia without any coloboma. Both eyes had mild corneal vascularisation with limbal stem cell deficiency. A diagnosis of congenital cataracts, megalocornea, limbal stem cell deficiency and inferior lenticular coloboma in the right eye was made. The patient underwent cataract surgery with aniridia intraocular lens in the right eye with a good visual outcome. Best-corrected visual acuity was improved to 20/40.