Alpha synuclein-mediated cytoskeletal dysfunction impairs myelination in human oligodendrocytes
Oligodendroglial alpha-synuclein (aSyn) deposits are a key feature in the atypical parkinsonian disorder, multiple system atrophy (MSA) linked to profound myelin loss and neurodegeneration while precise cellular and molecular mechanisms remain unclear. We generated human oligodendrocytes (hOLs) from induced pluripotent stem cells to investigate the impact of aSyn on oligodendroglial morphology, differentiation, and function. We observed an aSyn-induced myelinogenic dysfunction characterized by impaired oligodendroglial process outgrowth, altered cell shape, and increased perinuclear accumulation of the tubulin polymerization promoting protein TPPP/p25α. These changes were associated with a reduced capacity to ensheath axons and were linked to compromised actin remodeling machinery. Actin imbalances were confirmed in post-mortem putaminal tissue from MSA patients. Treatment with a rho-associated protein kinase inhibitor rescued oligodendroglial process formation and improved ensheathment in aSyn-expressing hOLs. Our work emphasizes the aSyn-mediated interference with actin dynamics as a key pathogenic mechanism in MSA, pointing toward a novel therapeutic target for improving myelin maintenance.
Authors
- Aron Koller (ORCID: https://orcid.org/0009-0004-1898-0374)
- Isabell Karnatz
- Marcus Himmler (ORCID: https://orcid.org/0000-0002-6016-9911)
- Alana Hoffmann (ORCID: https://orcid.org/0000-0002-5476-1038)
- Jürgen Winkler (ORCID: https://orcid.org/0000-0003-0630-9204)
- Anthony Varghese (ORCID: https://orcid.org/0000-0002-2923-6389)
- Farina Windener
- Kristina Battis
- Tanja Kuhlmann (ORCID: https://orcid.org/0000-0002-0174-5042)
- Wei Xiang (ORCID: https://orcid.org/0000-0002-0347-619X)
- Friederike Zunke (ORCID: https://orcid.org/0000-0002-0408-6388)
- Jeanette Wihan (ORCID: https://orcid.org/0000-0003-1534-0107)
- Dirk W. Schubert (ORCID: https://orcid.org/0000-0002-3021-4726)
Institutions
- University of Toronto (CA)
- Saarland University (DE)
Publication Details
- Journal
- Acta Neuropathologica
- Published
- 2025-09-19
- DOI
- https://doi.org/10.1007/s00401-025-02933-z
- Primary Topic
- Parkinson's Disease Mechanisms and Treatments
- Type
- article
- Field-Weighted Citation Impact
- 0.00
Funders
- European Federation of Pharmaceutical Industries and Associations
- European Commission
- Deutsche Forschungsgemeinschaft