Association of Diaphragm Involvement Assessed by Ultrasound With Disease Severity in Facioscapulohumeral Muscular Dystrophy

Ultrasound parameters, including V<sub>VS</sub> and ECHO-MRR, are informative for assessing diaphragm involvement and respiratory involvement in FSHD1. This knowledge establishes diaphragm ultrasound parameters as potential biomarkers of FSHD1 disease severity in upcoming clinical trials.

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Publication Details

Journal
Journal of Cachexia Sarcopenia and Muscle
Published
2025-09-12
DOI
https://doi.org/10.1002/jcsm.70057
Citations
1
Primary Topic
Chronic Obstructive Pulmonary Disease (COPD) Research
Type
article
Field-Weighted Citation Impact
1.52
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article

Association of Diaphragm Involvement Assessed by Ultrasound With Disease Severity in Facioscapulohumeral Muscular Dystrophy

Fuze Zheng, Qifang He, Min‐Ting Lin, Jie Chen et al.
1 citations
Journal of Cachexia Sarcopenia and Muscle
Chronic Obstructive Pulmonary Disease (COPD) Research
1.52
article

Association of Diaphragm Involvement Assessed by Ultrasound With Disease Severity in Facioscapulohumeral Muscular Dystrophy

Fuze Zheng, Qifang He, Min‐Ting Lin, Jie Chen, Liulei Wu, Liangliang Qiu, Xiaodan Lin, Lin Feng, Jing Xu, Long Chen, Li Chen, Ning Wang, Xin Lin, Zhiqiang Wang, Kang Li, Xiang Xu, Minghui Zeng, Guorong Lyu, Ying Zheng
article en
1 citations

Abstract

Ultrasound parameters, including V<sub>VS</sub> and ECHO-MRR, are informative for assessing diaphragm involvement and respiratory involvement in FSHD1. This knowledge establishes diaphragm ultrasound parameters as potential biomarkers of FSHD1 disease severity in upcoming clinical trials.

Journal of Cachexia Sarcopenia and MuscleVol. 16(5)
Fujian Medical University (CN), Quanzhou Normal University (CN), Quzhou College of Technology (CN), First Affiliated Hospital of Fujian Medical University (CN), Second Affiliated Hospital of Fujian Medical University (CN)
Openalex Percentile: Top 14%
Chronic Obstructive Pulmonary Disease (COPD) Research
1.52
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Association of Diaphragm Involvement Assessed by Ultrasound With Disease Severity in Facioscapulohumeral Muscular Dystrophy — Fuze Zheng, Qifang He, et al. · Journal of Cachexia Sarcopenia and Muscle (2025) | TGRS Research Map | TGRS