Association of Diaphragm Involvement Assessed by Ultrasound With Disease Severity in Facioscapulohumeral Muscular Dystrophy
Ultrasound parameters, including V<sub>VS</sub> and ECHO-MRR, are informative for assessing diaphragm involvement and respiratory involvement in FSHD1. This knowledge establishes diaphragm ultrasound parameters as potential biomarkers of FSHD1 disease severity in upcoming clinical trials.
Authors
- Fuze Zheng
- Qifang He
- Min‐Ting Lin
- Jie Chen (ORCID: https://orcid.org/0000-0002-0110-1706)
- Liulei Wu
- Liangliang Qiu (ORCID: https://orcid.org/0000-0002-1983-3331)
- Xiaodan Lin
- Lin Feng (ORCID: https://orcid.org/0000-0001-6461-5838)
- Jing Xu (ORCID: https://orcid.org/0000-0003-0070-0907)
- Long Chen (ORCID: https://orcid.org/0000-0002-7347-3074)
- Li Chen (ORCID: https://orcid.org/0000-0003-4752-4314)
- Ning Wang (ORCID: https://orcid.org/0000-0002-9655-9735)
- Xin Lin (ORCID: https://orcid.org/0000-0001-6913-4654)
- Zhiqiang Wang (ORCID: https://orcid.org/0000-0003-2796-6318)
- Kang Li (ORCID: https://orcid.org/0000-0002-1468-2220)
- Xiang Xu (ORCID: https://orcid.org/0000-0003-3279-598X)
- Minghui Zeng (ORCID: https://orcid.org/0000-0002-6055-6495)
- Guorong Lyu (ORCID: https://orcid.org/0000-0002-2160-0115)
- Ying Zheng (ORCID: https://orcid.org/0000-0002-5264-6431)
Institutions
- Fujian Medical University (CN)
- Quanzhou Normal University (CN)
- Quzhou College of Technology (CN)
- First Affiliated Hospital of Fujian Medical University (CN)
- Second Affiliated Hospital of Fujian Medical University (CN)
Publication Details
- Journal
- Journal of Cachexia Sarcopenia and Muscle
- Published
- 2025-09-12
- DOI
- https://doi.org/10.1002/jcsm.70057
- Citations
- 1
- Primary Topic
- Chronic Obstructive Pulmonary Disease (COPD) Research
- Type
- article
- Field-Weighted Citation Impact
- 1.52