Varied Presentations of Arterial Events in Vascular Ehlers-Danlos Syndrome
Spontaneous arterial aneurysms and dissections are relatively common in patients with vascular Ehlers-Danlos syndrome, and arterial rupture accounts for most deaths. Members of the Aortic and Vascular Disease Clinic at UTHealth Houston hold a monthly conference that includes cardiothoracic and vascular surgeons, cardiologists, geneticists, radiologists, and pathologists to formulate multidisciplinary approaches for the management of complex cases. In this case series, we highlight the variable presentations and clinical evolution of complex aortic and vascular disease due to vascular Ehlers-Danlos syndrome.
Authors
- Alana C. Cecchi (ORCID: https://orcid.org/0000-0002-9588-8705)
- Siddharth K. Prakash (ORCID: https://orcid.org/0000-0001-6341-9624)
- Salman Arain (ORCID: https://orcid.org/0000-0002-5810-4991)
- L. Maximilian Buja (ORCID: https://orcid.org/0000-0001-8386-7029)
- Anthony L. Estrera (ORCID: https://orcid.org/0000-0001-6594-6647)
- Sharon Zachariah (ORCID: https://orcid.org/0009-0008-0260-308X)
- Rana O. Afifi (ORCID: https://orcid.org/0000-0002-0152-2228)
- Thanila A. Macedo (ORCID: https://orcid.org/0000-0003-3556-1556)
- Dianna M. Milewicz (ORCID: https://orcid.org/0000-0002-7806-0068)
- Bihong Zhao (ORCID: https://orcid.org/0000-0002-1444-0686)
- Sara Mansoorshahi (ORCID: https://orcid.org/0009-0002-9668-5640)
- Akiko Tanaka
- Milan Jaiswal
- Gustavo S. Oderich
Institutions
- The University of Texas Health Science Center (US)
- The University of Texas Health Science Center at Houston (US)
Publication Details
- Journal
- JACC Case Reports
- Published
- 2025-09-12
- DOI
- https://doi.org/10.1016/j.jaccas.2025.105424
- Primary Topic
- Connective tissue disorders research
- Type
- article
- Field-Weighted Citation Impact
- 0.00