Cerebrospinal Fluid Otorrhea from Congenital Inner Ear Malformations: Clinical Experience and Lessons of a Case Report

<i>Objective:</i> To summarize the experience in diagnosis and treatment of patients with cerebrospinal fluid otorrhea secondary to congenital inner ear malformations and surgical operation treatment methods. <i>Methods: </i>The clinical data of a patient with cerebrospinal fluid otorrhea secondary to congenital inner ear malformations, Mondini dysplasia, was retrospectively analyzed, and the cerebrospinal otorrhea packing repair was performed transcanal endoscopic. <i>Results:</i> The patient was misdiagnosed and improperly treated before the surgery. The patient was successfully treated with transcanal endoscopic surgical exploration revealed a missing leak in the patella floor plate, patellar muscle and myofascial membrane were used to pack the inner ear, seal the vestibular window. There was no cerebrospinal fluid otorrhea and recurrence of meningitis after postoperative follow-up of 1 year. <i>Conclusions:</i> It reminds that patient who has hearing impairment associated with recurrent meningitis, otorrhea, or rhinorrhea should be evaluated for the possibility of this congenital dysplasia, and early diagnosis and prompt surgical intervention may prevent further episodes. It a condition that requires elevated clinical vigilance.