Diagnosis and Management of a Child With Primary Pancreatic Neuroblastoma: Case Report of a Common Malignancy at a Rare Site

Pediatric pancreatic neuroblastoma is a rare cancer in children, with only limited cases available in the literature. We report a case of a 4-year-old girl diagnosed with high-risk pancreatic neuroblastoma. The girl was treated with induction chemotherapy followed by autologous stem cell transplant and maintenance with 13-cis-retinoic acid. Surgery and radiotherapy were not feasible due to the very small size of the mass postinduction, the location of the tumor, and the expected toxicities. The girl completed treatment successfully and is now 1 and a half years postautologous stem cell transplant without any evidence of disease.