Mammary-Like Tumor of the Vulva: Immunostaining and Hormone Receptor Status Guide

The aim of this article is to present a rare case of a patient with Vulvar Adnexal Carcinoma, Mammary Type (VACMT). Following this unusual diagnosis, we wish to delineate our diagnostic and treatment course and clinical outcomes. We strongly support a multi-disciplinary approach when dealing with this rare type of vulvar cancer. In addition, the histologic findings of this rare malignancy are fully analyzed and described. A thorough literature review of previous cases described in literature was conducted according to the PRISMA guidelines. We have identified and highlighted key features and specific histological markers suggestive of this diagnosis and crucial in order to differentiate and diagnose this rare type of malignancy. Finally, we would like to share our experience with the chosen mode of treatment in this patient and encourage further research and sharing of knowledge among different specialists involved in the treatment of this fascinating rare tumors.