Mucociliary and cough clearance in primary ciliary dyskinesia as affected by mutations in <i>RSPH1</i> or <i>DNAH5</i>
The results confirm impaired MCC in people with PCD of both genotypes. However, in this small cohort, the results suggest cough clearance may differ between these two genotypes.
Authors
- Margaret W. Leigh (ORCID: https://orcid.org/0000-0002-6420-2459)
- Michael Knowles (ORCID: https://orcid.org/0000-0001-7396-7966)
- Agathe Ceppe (ORCID: https://orcid.org/0009-0008-9031-1166)
- Thomas W. Ferkol (ORCID: https://orcid.org/0000-0003-2477-9357)
- Kirby L. Zeman (ORCID: https://orcid.org/0000-0003-2536-396X)
- William D. Bennett (ORCID: https://orcid.org/0000-0002-6054-0768)
- Chelsea Taylor (ORCID: https://orcid.org/0000-0002-1635-4167)
- Lawrence E. Ostrowski (ORCID: https://orcid.org/0000-0002-7558-6603)
- S. Abu-Nasser
- Maimoona A. Zariwala
- Kenneth N. Olivier
Institutions
- University of North Carolina at Chapel Hill (US)
- Lung Institute (US)
Publication Details
- Journal
- ERJ Open Research
- Published
- 2025-09-04
- DOI
- https://doi.org/10.1183/23120541.00681-2025
- Citations
- 1
- Primary Topic
- Cystic Fibrosis Research Advances
- Type
- article
- Field-Weighted Citation Impact
- 1.52
Funders
- National Heart, Lung, and Blood Institute