Congenitally Corrected Transposition of Great Arteries in a Young Adult: A Case Report

Congenitally Corrected Transposition of the Great Arteries (ccTGA) is a rare congenital cardiac anomaly characterised by atrioventricular and ventriculoarterial discordance, comprising less than 0.05% of all congenital heart diseases. While often associated with abnormalities such as Ventricular Septal Defect (VSD), pulmonary obstruction, coarctation, and Ebstein anomaly, ccTGA can also occur as an isolated defect. Such cases may remain asymptomatic for decades and are sometimes discovered incidentally. We present a case of a 26-year-old asymptomatic male diagnosed with ccTGA during an evaluation for inguinal hernia surgery. The patient’s only complaint was occasional palpitations. Electrocardiography revealed Complete Heart Block (CHB), which was confirmed by echocardiography and coronary Computed Tomography (CT) angiography, showing typical findings of ccTGA. The Right Ventricle (RV) had a reduced ejection fraction of 40-45%, with mild regurgitation of the tricuspid and aortic valves. Pacemaker implantation was recommended for the management of CHB. This case highlights the importance of early recognition of ccTGA-associated complications such as CHB and underscores the need for regular follow-up to monitor for Heart Failure (HF) and other late sequelae.