Pleuroparenchymal fibroelastosis: review of 81 cases
Idiopathic and secondary PPFE differ in FVC decline but not in mortality risk. Familial and autoimmune conditions are the most common secondary causes.
Authors
- Eunhee E. Yi
- Thomas E. Hartman (ORCID: https://orcid.org/0000-0002-7857-7024)
- Allison LeMahieu (ORCID: https://orcid.org/0000-0003-1554-795X)
- Wigdan Farah (ORCID: https://orcid.org/0000-0002-2886-341X)
- Jay Hoon Ryu (ORCID: https://orcid.org/0000-0002-9576-2272)
- Misbah Baqir (ORCID: https://orcid.org/0000-0002-5632-8131)
Institutions
- Mayo Clinic (US)
- WinnMed (US)
- Mayo Clinic in Arizona (US)
- Mayo Clinic in Florida (US)
Publication Details
- Journal
- Expert Review of Respiratory Medicine
- Published
- 2025-08-29
- DOI
- https://doi.org/10.1080/17476348.2025.2555079
- Primary Topic
- Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
- Type
- article
- Field-Weighted Citation Impact
- 0.00