IgG4-related disease presenting with retroperitoneal fibrosis and hypertrophic spinal pachymeningitis: a rare case report and literature review

This rare case underscores the importance of integrating clinical, radiological, and histopathological findings to diagnose HSP and RPF, particularly in the context of IgG4-RD. Early multidisciplinary management is critical to improving outcomes.

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Publication Details

Journal
Frontiers in Immunology
Published
2025-08-29
DOI
https://doi.org/10.3389/fimmu.2025.1619756
Citations
1
Primary Topic
IgG4-Related and Inflammatory Diseases
Type
article
Field-Weighted Citation Impact
1.67

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article

IgG4-related disease presenting with retroperitoneal fibrosis and hypertrophic spinal pachymeningitis: a rare case report and literature review

Jingru Ren, Jianchun Wang, Ran Liu, Hongzhou Duan et al.
1 citations
Frontiers in Immunology
IgG4-Related and Inflammatory Diseases
1.67
article

IgG4-related disease presenting with retroperitoneal fibrosis and hypertrophic spinal pachymeningitis: a rare case report and literature review

Jingru Ren, Jianchun Wang, Ran Liu, Hongzhou Duan, Zhenyu Niu, Siwei Chen, Feifan Xu, Juan Zhao, Feng Gao, Haoze Zhang
article en
1 citations

Abstract

This rare case underscores the importance of integrating clinical, radiological, and histopathological findings to diagnose HSP and RPF, particularly in the context of IgG4-RD. Early multidisciplinary management is critical to improving outcomes.

Frontiers in ImmunologyVol. 16
Peking University (CN), Peking University First Hospital (CN)
National Natural Science Foundation of China
Openalex Percentile: Top 14%
IgG4-Related and Inflammatory Diseases
1.67
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IgG4-related disease presenting with retroperitoneal fibrosis and hypertrophic spinal pachymeningitis: a rare case report and literature review — Jingru Ren, Jianchun Wang, et al. · Frontiers in Immunology (2025) | TGRS Research Map | TGRS