A Rare Case of Undiagnosed Anomalous Right Coronary Artery From the Pulmonary Artery in an Asymptomatic Seven-Year-Old
Anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA) is an extremely rare congenital coronary artery anomaly. Diagnosis is often made incidentally when evaluating for a murmur or other congenital heart disease. The ARCAPA may present with right heart failure and/or sudden cardiac death and surgical repair is recommended once the diagnosis is made.A seven-year-old child previously diagnosed with small ventricular septal defects presented to our cardiology clinic as a new patient. Echocardiogram revealed suspicion of a coronary anomaly and computed tomography angiography (CTA) confirmed a diagnosis of ARCAPA. She underwent successful surgical reimplantation of the anomalous right coronary artery and made an excellent recovery.This case highlights the importance of maintaining a high index of suspicion for coronary anomalies and strongly considering CTA in patients with imaging findings or symptoms consistent with ARCAPA.
Authors
- Olga Salazar
- Caitlin Heyden
- Jill M. Sullivan
- Dennis Mello
- Randy M. Stevens (ORCID: https://orcid.org/0000-0001-8454-6956)
- James Wiley
Institutions
- University of Connecticut (US)
- Connecticut Children's Medical Center (US)
Publication Details
- Journal
- World Journal for Pediatric and Congenital Heart Surgery
- Published
- 2025-08-25
- DOI
- https://doi.org/10.1177/21501351251361502
- Primary Topic
- Coronary Artery Anomalies
- Type
- article
- Field-Weighted Citation Impact
- 0.00