IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report

IgG4-related disease (IgG4-RD) is a rare autoimmune disease which can affect almost any organ. We present a case of IgG4-RD, which manifested as chronic autoimmune pancreatitis with pancreatic insufficiency, severe malnutrition, autoimmune sialadenitis, and cholangitis. After the administration of prednisolone and mycophenolate mofetil, the patient's condition improved significantly.

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Publication Details

Journal
Acta medica Lituanica
Published
2025-08-25
DOI
https://doi.org/10.15388/amed.2025.32.2.11
Primary Topic
IgG4-Related and Inflammatory Diseases
Type
article
Field-Weighted Citation Impact
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article

IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report

Augustina Tumelytė, Paulina Tekoriutė, Limas Kupčinskas, Vytautas Rimkus
Acta medica Lituanica
IgG4-Related and Inflammatory Diseases
article

IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report

Augustina Tumelytė, Paulina Tekoriutė, Limas Kupčinskas, Vytautas Rimkus
article en

Abstract

IgG4-related disease (IgG4-RD) is a rare autoimmune disease which can affect almost any organ. We present a case of IgG4-RD, which manifested as chronic autoimmune pancreatitis with pancreatic insufficiency, severe malnutrition, autoimmune sialadenitis, and cholangitis. After the administration of prednisolone and mycophenolate mofetil, the patient's condition improved significantly.

Acta medica LituanicaVol. 32(2)
Lithuanian University of Health Sciences (LT)
Openalex Percentile: Top 66%
IgG4-Related and Inflammatory Diseases
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