IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report
IgG4-related disease (IgG4-RD) is a rare autoimmune disease which can affect almost any organ. We present a case of IgG4-RD, which manifested as chronic autoimmune pancreatitis with pancreatic insufficiency, severe malnutrition, autoimmune sialadenitis, and cholangitis. After the administration of prednisolone and mycophenolate mofetil, the patient's condition improved significantly.
Authors
- Augustina Tumelytė
- Paulina Tekoriutė
- Limas Kupčinskas
- Vytautas Rimkus
Institutions
- Lithuanian University of Health Sciences (LT)
Publication Details
- Journal
- Acta medica Lituanica
- Published
- 2025-08-25
- DOI
- https://doi.org/10.15388/amed.2025.32.2.11
- Primary Topic
- IgG4-Related and Inflammatory Diseases
- Type
- article
- Field-Weighted Citation Impact
- 0.00