Paracentral Acute Middle Maculopathy in Atrial Septal Defect

Paracentral acute middle maculopathy is an ischemic disease of the posterior pole of the retina characterised by the sudden appearance of a central scotoma caused by small infarcts in its inner layers. Optical coherence tomography highlights these lesions as typical hyperreflective bands involving the inner retinal layers. This report presents two cases of paracentral acute middle maculopathy associated with the presence of an atrial septal defect. The discovery of these retinal microinfarcts, especially in young patients with a history of migraine with aura, requires neurocardiological investigations to rule out the presence of an atrial septal defect and any cerebral ischemic lesions.