Dedifferentiated liposarcoma with low-grade fibromyxoid sarcoma and inflammatory myofibroblastic tumor: A case report and literature review
This case underscores critical clinical lessons: diagnostic vigilance is paramount when assessing sarcomas with mixed morphological patterns, given that DDLPS may closely mimic IMT or LGFMS. To prevent misdiagnosis, a systematic diagnostic approach radiological, immunohistochemistry, and confirmatory molecular testing is essential. Therapeutic management relies on complete surgical resection, with adjuvant therapy decisions guided by multidisciplinary evaluation. Long-term surveillance remains necessary due to recognized risks of late recurrence in retroperitoneal DDLPS, mandating sustained follow-up.
Authors
- Yuzhen Huang (ORCID: https://orcid.org/0000-0002-9536-7918)
- Lixia Zeng
- Xiaoyu Chen (ORCID: https://orcid.org/0000-0002-0492-7589)
- Yun Ma (ORCID: https://orcid.org/0000-0001-5958-0183)
- Jing Huang (ORCID: https://orcid.org/0000-0002-5950-4612)
Institutions
- Guangxi Medical University (CN)
Publication Details
- Journal
- Medicine
- Published
- 2025-08-15
- DOI
- https://doi.org/10.1097/md.0000000000043806
- Primary Topic
- Sarcoma Diagnosis and Treatment
- Type
- article
- Field-Weighted Citation Impact
- 0.00