Transthyretin variant cerebral amyloid angiopathy fulfilling the modified Boston criteria: Retrospective data from the Bicêtre hospital cohort
ATTRv-related CAA should be considered in case of CAA with suggestive systemic features or familial history, as specific treatments and genetic counseling now exist for ATTRv. Conversely, CNS symptoms and brain MRI abnormalities should be sought in ATTRv patients.
Authors
- Cécile Cauquil
- Luisa Gorza (ORCID: https://orcid.org/0000-0003-4897-400X)
- Christian Denier (ORCID: https://orcid.org/0000-0002-2087-5563)
- Claire Ancelet (ORCID: https://orcid.org/0000-0002-0205-5721)
- M. Babín
- Céline Labeyrie (ORCID: https://orcid.org/0000-0001-9765-709X)
- G. Nasser
- J-B Brunet de Courssou
Institutions
- Université Paris-Saclay (FR)
- Assistance Publique – Hôpitaux de Paris (FR)
- Hôpital Foch (FR)
- Bicêtre Hospital (FR)
Publication Details
- Journal
- Revue Neurologique
- Published
- 2025-08-14
- DOI
- https://doi.org/10.1016/j.neurol.2025.07.012
- Citations
- 1
- Primary Topic
- Amyloidosis: Diagnosis, Treatment, Outcomes
- Type
- article
- Field-Weighted Citation Impact
- 0.81