Chronic thromboembolic pulmonary hypertension: a case-based discussion of current management and latest guidelines

Purpose of review: Frequently underdiagnosed, chronic thromboembolic pulmonary hypertension (CTEPH) is associated with high morbidity and mortality. We highlight recent advancements in evaluation and management. Recent findings: This study focuses on a case-based management approach for CTEPH. It outlines the initial evaluation, treatment approach, and the importance of timely intervention. Although a surgical approach can potentially be curative, we discuss the role of medical management and balloon pulmonary angioplasty (BPA). Summary: This review highlights the importance of early recognition, diagnostic evaluation, and current evidence-based multidisciplinary management of patients with CTEPH. Keywords: Chronic thromboembolic pulmonary hypertension, pulmonary endarterectomy, balloon pulmonary angioplasty, riociguat.