Anterior cervical hypertrichosis associated with speckled lentiginous nevus

Anterior cervical hypertrichosis (ACH), or “hairy throat,” is a rare form of localized hypertrichosis characterized by a tuft of terminal hair on the anterior neck, usually just above the laryngeal prominence. It is usually seen as an isolated finding, but may be associated with systemic disorders such as neurologic abnormalities. We report the case of an 11-year-old girl who presented with ACH associated with speckled lentiginous nevus.