American College of Rheumatology Guidance Statement for Diagnosis and Management of <scp>VEXAS</scp> Developed by the International <scp>VEXAS</scp> Working Group Expert Panel
This work marks the first formal international consensus guidance for VEXAS and is intended to be used as a resource for clinicians seeking to understand the disease and its management.
Authors
- Sinisa Savic (ORCID: https://orcid.org/0000-0001-7910-0554)
- Yohei Kirino (ORCID: https://orcid.org/0000-0002-9488-661X)
- Lauren M. Madigan (ORCID: https://orcid.org/0000-0001-5659-5734)
- Marie Robin (ORCID: https://orcid.org/0000-0003-1388-9876)
- Matthew J. Koster (ORCID: https://orcid.org/0000-0002-2895-6755)
- Yervand Hakobyan (ORCID: https://orcid.org/0000-0002-9074-7831)
- Olivier Kosmider (ORCID: https://orcid.org/0000-0002-6021-4057)
- Franco Franceschini (ORCID: https://orcid.org/0000-0003-3678-6124)
- Elisa Diral (ORCID: https://orcid.org/0000-0002-4994-7719)
- Henrique Coelho (ORCID: https://orcid.org/0000-0003-0909-9601)
- Francesca Crisafulli (ORCID: https://orcid.org/0000-0003-0319-1538)
- Alessandro Tomelleri (ORCID: https://orcid.org/0000-0002-5440-2078)
- Corrado Campochiaro (ORCID: https://orcid.org/0000-0001-6806-3794)
- G. Urbanski (ORCID: https://orcid.org/0000-0001-5719-8423)
- Hideaki Nakajima (ORCID: https://orcid.org/0000-0002-8967-4954)
- Marcin Milchert (ORCID: https://orcid.org/0000-0002-0943-8768)
- François Chasset (ORCID: https://orcid.org/0000-0003-2580-8607)
- Annmarie Bosco
- Chiara M. Cattaneo (ORCID: https://orcid.org/0000-0003-0031-3237)
- Katherine R. Calvo (ORCID: https://orcid.org/0000-0002-0771-4191)
- Austin Kulasekararaj (ORCID: https://orcid.org/0000-0003-3180-3570)
- Chiara Marvisi (ORCID: https://orcid.org/0000-0001-7027-1410)
- R. Bourguiba (ORCID: https://orcid.org/0000-0002-7352-9074)
- Ewa Więsik–Szewczyk (ORCID: https://orcid.org/0000-0001-8509-4453)
- Anthony M. Sammel (ORCID: https://orcid.org/0000-0003-3641-796X)
- Stéphanie Ducharme‐Bénard (ORCID: https://orcid.org/0000-0003-1555-3815)
- Hiroyoshi Kunimoto
- Emma M. Groarke (ORCID: https://orcid.org/0000-0002-4648-5926)
- David B. Beck (ORCID: https://orcid.org/0000-0002-5884-6231)
- Yvan Jamilloux (ORCID: https://orcid.org/0000-0001-5249-3650)
- Carmelo Gurnari (ORCID: https://orcid.org/0000-0001-6829-5544)
- Frédéric Vandergheynst
- Sara Moráis (ORCID: https://orcid.org/0000-0003-4266-4457)
- Abraham Rutgers (ORCID: https://orcid.org/0000-0002-1641-6890)
- Juan I. Aróstegui (ORCID: https://orcid.org/0000-0003-4757-504X)
- H. Mann (ORCID: https://orcid.org/0000-0002-4243-235X)
- Thibault Comont (ORCID: https://orcid.org/0000-0002-6891-9238)
- Jörg D. Seebach (ORCID: https://orcid.org/0000-0001-5748-4577)
- Raquel Faria (ORCID: https://orcid.org/0000-0002-2956-1966)
- Mrinal M. Patnaik (ORCID: https://orcid.org/0000-0001-6998-662X)
- Katja Sockel (ORCID: https://orcid.org/0000-0003-1732-7299)
- Ciprian Jurcuț (ORCID: https://orcid.org/0000-0001-9613-7420)
- Catherine Cargo (ORCID: https://orcid.org/0000-0002-5185-0190)
- Micol Frassi
- Pierre Sujobert (ORCID: https://orcid.org/0000-0003-1724-4792)
- Bhavisha A. Patel (ORCID: https://orcid.org/0000-0002-2974-7701)
- Marcela A. Ferrada (ORCID: https://orcid.org/0000-0003-3256-3273)
- Francesco Muratore (ORCID: https://orcid.org/0000-0003-0362-2668)
- A. Mékinian (ORCID: https://orcid.org/0000-0003-2849-3049)
- Peter C. Grayson (ORCID: https://orcid.org/0000-0002-8269-9438)
- Benjamin Terrier (ORCID: https://orcid.org/0000-0001-6612-7336)
- Carlo Salvarani (ORCID: https://orcid.org/0000-0003-3708-3148)
- Romana Vieira
- Pierre Fenaux
- Luísa Regadas
- David S. Viswanatha
- Sophie Georgin‐Lavaille
- Mael Heilblig
Institutions
- Tunis University (TN)
- University of Rome Tor Vergata (IT)
- University of Modena and Reggio Emilia (IT)
- University of Maryland, Baltimore (US)
- Centre National de la Recherche Scientifique (FR)
- National Institutes of Health (US)
- University of Leeds (GB)
- New South Wales Department of Health (AU)
- Cleveland Clinic (US)
- Université Libre de Bruxelles (BE)
- A. Alikhanyan National Laboratory (AM)
- Mayo Clinic (US)
- University Medical Center Groningen (NL)
- Ministry of National Defense (KR)
- Université Toulouse III - Paul Sabatier (FR)
- Vita-Salute San Raffaele University (IT)
- Inserm (FR)
- King's College - North Carolina (US)
- German Cancer Research Center (DE)
- University of California, San Francisco (US)
- Universidade do Porto (PT)
- Université Paris Cité (FR)
- Charles University (CZ)
- University of Utah (US)
- St James's University Hospital (GB)
- University of Utah Hospital (US)
- Centre Hospitalier Universitaire de Toulouse (FR)
- UNSW Sydney (AU)
- National Institute for Health and Care Research (GB)
- Sorbonne Université (FR)
- National Institute of Arthritis and Musculoskeletal and Skin Diseases (US)
- Hôpital de la Croix-Rousse (FR)
- Städtisches Klinikum Dresden (DE)
- Azienda Sanitaria Unità Locale di Reggio Emilia (IT)
- Institute of Rheumatology (CZ)
- Hôpital Cochin (FR)
- Assistance Publique – Hôpitaux de Paris (FR)
- Hôpital régional (CH)
- Emergency University (US)
- Hospices Civils de Lyon (FR)
- Hôpital Saint-Antoine (FR)
- Azienda Socio Sanitaria Territoriale degli Spedali Civili di Brescia (IT)
- Center for Human Genetics (US)
- University Hospital of Geneva (CH)
- National Heart, Lung, and Blood Institute (US)
- Prince of Wales Hospital (AU)
- Administração Regional de Saúde de Lisboa e Vale do Tejo (PT)
- Centre Hospitalier Universitaire d'Angers (FR)
- Hôpital Lyon Sud (FR)
- NIHR Leeds Musculoskeletal Biomedical Research Unit (GB)
- Hospital Clínic de Barcelona (ES)
- Mayo Clinic in Arizona (US)
- Sydney Children's Hospital (AU)
- Hospital de Santo António (PT)
- IRCCS Ospedale San Raffaele (IT)
- Central Clinical Hospital (PL)
- Hôpital du Sacré-Cœur de Montréal (CA)
- Centro Hospitalar de Vila Nova de Gaia (PT)
- Institut Cochin (FR)
- Hôpital Saint-Louis (FR)
- Mayo Clinic in Florida (US)
- Istituti di Ricovero e Cura a Carattere Scientifico (IT)
- King's College Hospital (GB)
- Centro Hospitalar do Porto (PT)
- Consorci Institut D'Investigacions Biomediques August Pi I Sunyer (ES)
- Hôpital Tenon (FR)
- Istituto di Ricovero e Cura a Carattere Scientifico San Raffaele (IT)
- Deutsches Konsortium für Translationale Krebsforschung (DE)
- New York University (US)
- Tunis El Manar University (TN)
- Universitat de Barcelona (ES)
- Technische Universität Dresden (DE)
- Pomeranian Medical University (PL)
- University of Brescia (IT)
- Neuroscience Research Australia (AU)
- Yokohama City University (JP)
Publication Details
- Journal
- Arthritis & Rheumatology
- Published
- 2025-08-11
- DOI
- https://doi.org/10.1002/art.43287
- Citations
- 12
- Primary Topic
- Otitis Media and Relapsing Polychondritis
- Type
- article
- Field-Weighted Citation Impact
- 20.02
Funders
- Ministerstvo Zdravotnictví Ceské Republiky