Administrative coding for alpha-1 antitrypsin deficiency including the pi*ZZ phenotype is accurate in Sweden
In a tertiary care setting, the validity of ICD-10 codes for AATD is excellent. The PPV of these codes for delineating the Pi*ZZ-phenotype is high in children but requires an algorithm in adults with coding for E880B in outpatients.
Authors
- Axel Wester (ORCID: https://orcid.org/0000-0003-3634-6591)
- Susanne Ullman
- Hannes Hagström (ORCID: https://orcid.org/0000-0002-8474-1759)
- Jonas Filip Ludvigsson (ORCID: https://orcid.org/0000-0003-1024-5602)
- Staffan Wåhlin (ORCID: https://orcid.org/0000-0002-5985-9464)
- Joost Boeckmans (ORCID: https://orcid.org/0000-0001-8399-5872)
Institutions
- Karolinska University Hospital (SE)
- Vrije Universiteit Brussel (BE)
- Karolinska Institutet (SE)
- Örebro University Hospital (SE)
- Columbia College (CA)
- Royal College of Physicians (GB)
- Columbia University (US)
Publication Details
- Journal
- Scandinavian Journal of Gastroenterology
- Published
- 2025-08-11
- DOI
- https://doi.org/10.1080/00365521.2025.2544310
- Primary Topic
- Peptidase Inhibition and Analysis
- Type
- article
- Field-Weighted Citation Impact
- 0.00