Early Treatment With Intravenous Immunoglobulins and Outcomes of Patients With Anti-IgLON5 Disease

In this study, early initiation of intravenous immunoglobulins (within the first year of onset) was associated with favorable long-term outcomes and improved survival in anti-IgLON5 disease. Larger prospective studies are needed to validate this finding.

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Publication Details

Journal
JAMA Neurology
Published
2025-08-04
DOI
https://doi.org/10.1001/jamaneurol.2025.2574
Citations
3
Primary Topic
Autoimmune Neurological Disorders and Treatments
Type
article
Field-Weighted Citation Impact
4.17
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article

Early Treatment With Intravenous Immunoglobulins and Outcomes of Patients With Anti-IgLON5 Disease

Hauke Schneider, Morten Blaabjerg, Walid Fazeli, Henrik Rohner et al.
3 citations
JAMA Neurology
Autoimmune Neurological Disorders and Treatments
4.17
article

Early Treatment With Intravenous Immunoglobulins and Outcomes of Patients With Anti-IgLON5 Disease

Hauke Schneider, Morten Blaabjerg, Walid Fazeli, Henrik Rohner, Jan Lewerenz, Simon Schuster, Lucie de Azevedo, Olga Simova, Christian Hofmann, Marina Flotats‐Bastardas, Sonka Benesch, Rolf Kern, Philip Hillebrand, Sebastian Baatz, Ingo Kleiter, Felix Fischbach, Marie Madlener, Claudia Sommer, Robert Markewitz, Brigitte Wildemann, Caroline Giordana, Martin Lesser, Makbule Şenel, Felix von Podewils, Simone Zittel, Max Kaufmann, Hagen B. Huttner, Francesc Graus, Constanze Kerin, Jost Obrocki, Manuel Alexander Friese, Jan D. Lünemann, Lúcio Huebra Pimentel Filho, Luise Appeltshauser, Michael Nagel, Susanne Knake, Inmaculada Puertas, Caspar Seitz, Agnita J.W. Boon, Sigrid Reuter, Johannes Piepgras, Sarah Bernsen, Achim Berthele, Yavor Yalachkov, Birgit Berger, Sandra Stanković, Katharina Eisenhut, Simone C. Tauber, Frank Leypoldt, Lídia Sabater, Timo Deba, Fabian Möller, Hayrettin Tumani, Annette Baumgärtner, Annika Kather, Sonia Quintas, Christian Urbanek, Juan Carlos García‐Moncó, Mathias Fousse, Carlos Martínez Quesada, Martin Häusler, Regina Trollmann, Silke Tonner, Gernot Reimann, Peter Huppke, María Elena Erro, Markus Rauchenzauner, Tobias Freilinger, Chen Fei Ng, Niels Hansen, Inga Koneczny, Felix Rosenow, Aiden Haghikia, Anna Heidbreder, Johanna Maria Helena Rau, Michael Karenfort, Harald Prüß, Ulrich Hofstadt‐van Oy, Friedrich Ebinger, Yvette S. Crijnen, Dietrich Sturm, Sven Guenther Meuth, Tarsis Farias, Judith Wagner, Anja Tietz, Franziska E. Möllers, Marius Ringelstein, Verena Kraus, Christos Krogias, Franziska Thaler, Saskia Räuber, Sergio Castro‐Gomez, Mona Dreesmann, Christoph Kellinghaus, Yannic Saathoff, Stefan Bittner, Oliver Bähr, Marina Entscheva, Lara Zieger, Niklas Vogel, Mareike Jansen, Oliver Stammel, Britta Greshake, Sigrid Mues, Daniela Esser, Kerstin Hellwig, Jens Schmidt, Robert Weissert, Ruth Schilling, Thomas Grüter, Gian Maria Asioli, Anna Gorsler, Pasquale Nigro, Raphael Ribeiro Spera, Oliver Grauer, Kurt‐Wolfram Sühs, Kim Kristin Falk, Astrid Blaschek, Steffen Pfeuffer, Jan Wagner, Fedor Heidenreich, Karsten Witt, Dirk Fitzner, Joachim Havla, Raphael Reinecke, Kevin M. Rostasy, Karl‐Christian Thies, Josef Priller, Raphaela Heusgen, Maarten J. Titulaer, Sascha Berning, Friedemann Paul, Michael P. Malter, Andre Dik, Suzanne C. Franken, Juna M. de Vries, Alexander Emmer, Michelle Braun, Josep Dalmau, Henning Stolze, Thomas Schmitter, Juliane Spiegler, Corinna Trebst, Catharina C. Groß, Kathrin Doppler, Aleksandra Juranek, Ralf Gold, Antonio Martín‐Bastida, Paweł Tacik, Robert L. Berger, Kai Siebenbrodt, Laura Ehrhardt, Carolin Baade‐Büttner, Alexandra Philipsen, Mirjam Korporal‐Kuhnke, Stjepana Kovac, Martin Berghoff, Thomas Pfefferkorn, Maja Patalong‐Ogiewa, Nico Melzer, Thorleif Etgen, Christine Strippel, Robert Rehmann, Valentin Held, Peter Körtvélyessy, Justina Dargvainiene, Robert Handreka, Thilo van Eimeren, Javier Villacieros‐Álvarez, Marie‐Luise Mono, Loana Penner, Jens Schaumberg, Fatme Seval Ismail, Christian G. Bien, Thanos Tsaktanis, Romana Höftberger, Katya Kotschet, Federica Provini, Bettina Balint, Norbert Brüggemann, Gerd Meyer zu Hörste, Florian Then Bergh, Carsten Finke, Lena Kristina Pfeffer, Ina Reichen, Christoph Lehrich, Milene Schmitz, Jannis Justus Maaß, Ángela Milán-Tomás, Josef Schill, Franz Blaes, Carlos Ordás, Nils G. Margraf, Patrick Schramm, Daniel Rapp, Sven Jarius, Ellen Knierim, Sebastian Bauer, Dominique Endres, Til Menge, Andreas van Baalen, Anne‐Katrin Pröbstel, Tanja Kümpfel, Julian Dominik, Alexander Finke, Steffen Syrbe, G Seidel, David J. Pedrosa, Mosche Pompsch, Mateus Mistieri Simabukuro, Michael Adelmann, Marc Nikolaus, Marlene Tschernatsch, Tobias Baumgartner, Jens Harmel, Nicola Tambasco, Jonathan Wickel, Antonios Bayas, Antonia Harms, Ilya Ayzenberg, Christian Geis, Muriel Stoppe, Nele Retzlaff, Klarissa Hanja Stürner, Theodor Rüber, Robin W. van Steenhoven, Marco Gallus, Ruth Kerkhoff, Duygu Pul, Jaqueline Klausewitz, Chung Ha-Yeun, Andeas Linsa, Kristin Stefanie Melzer, Gesa Schreyer, Methap Türedi, Max Vogtmann, Kartharina Wurdack, Lena Edelhoff, Yetzenia Dubraska Haro Alizo, Jesús Jiménez, Mareike Schimmel, Frank Seifert, Stephan J. Rüegg, George Trendelenburg, Thomas Seifert‐Held, Andreas Binder, Carles Gaig, Armin Grau, Stefanie Becker, Stephan Schreiber, Frank Hoffmann, Corinna Bien, Sharon Veenbergen, Wolfgang Heide, M. M. Gebhard, Monika Meister, Ina Schröder, Jürgen Faiss, Alejandro Herrero-San Martín, Matthias von Mering, Andrea Kraft, Martina Jansen, Sven Ehrlich, Ina-Isabelle Schmütz, Amelie Bohn, Karin Storm van’s Gravesande, Klaus-Peter Wandinger, Markus Krämer, Andeas Steinbrecher, Julia Maren Decker, Gregor Kuhlenbäumer, Nieves Téllez, Felix F. Konen, Florian Schöberl, Daniel Bittner, Dominica Hudasch, Frank Kohlert, Anna-Katharina Mundorf, Philip Schwenkenbecher, Rem Vaizian, Njiku Melchior Wellmer, Julia Bierwith, Johanna-Maria Dietmaier, Jonas Marius, Alina Neffgen
article en
3 citations

Abstract

In this study, early initiation of intravenous immunoglobulins (within the first year of onset) was associated with favorable long-term outcomes and improved survival in anti-IgLON5 disease. Larger prospective studies are needed to validate this finding.

JAMA NeurologyVol. 82(10)
Innsbruck Medical University (AT), Universität Innsbruck (AT), Universität Ulm (DE), University of Münster (DE), Erasmus MC (NL), Universitätsklinikum Erlangen (DE), University Hospital Münster (DE), Centre for Biomedical Network Research on Rare Diseases (ES), University Hospital Schleswig-Holstein (DE), Hospital Clínic de Barcelona (ES), Navarrabiomed (ES), Kepler Universitätsklinikum (AT), Katholisches Klinikum Koblenz (DE), Klinikum Lippe (DE), Jena University Hospital (DE), Antea Group (France) (FR), St. Josef-Hospital (DE), Martha-Maria Hospital (DE), Consorci Institut D'Investigacions Biomediques August Pi I Sunyer (ES), Barcelona School of Economics (ES), Medical University of Vienna (AT), Ludwig-Maximilians-Universität München (DE), Ruhr University Bochum (DE), University of Lübeck (DE)
Good health and well-being
Openalex Percentile: Top 6%
Autoimmune Neurological Disorders and Treatments
4.17
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