Natural History of Primary Retroperitoneal Extra-Visceral Perivascular Epithelioid Cell Tumors (PEC): A Study from Transatlantic and Australasian Retroperitoneal Sarcoma Working Group (TARPSWG)
Retroperitoneal and abdominopelvic PEComas show distinct behaviors by subtype. PEComa NOS had the highest recurrence and mortality, sclerosing PEComa showed intermediate risk, and AML was indolent. Histological classification is essential for prognosis and management.
Authors
- David Gyorki (ORCID: https://orcid.org/0000-0002-3165-4694)
- Michael J. Wagner (ORCID: https://orcid.org/0000-0002-8812-1653)
- M Knoblauch
- Catherine Mitchell (ORCID: https://orcid.org/0000-0003-3069-6590)
- Eyal Mor (ORCID: https://orcid.org/0000-0002-3235-2946)
- Max Almond (ORCID: https://orcid.org/0000-0003-4133-312X)
- Giovanni Grignani (ORCID: https://orcid.org/0000-0001-5515-569X)
- Adam D. Barlow (ORCID: https://orcid.org/0000-0002-3925-5401)
- Carolyn Nessim (ORCID: https://orcid.org/0000-0002-0419-3511)
- Lee D. Cranmer (ORCID: https://orcid.org/0000-0002-7789-5442)
- Sameer Apte (ORCID: https://orcid.org/0000-0003-1099-8268)
- Alessandro Gronchi (ORCID: https://orcid.org/0000-0002-4703-3534)
- Markus Albertsmeier (ORCID: https://orcid.org/0000-0002-5028-5062)
- Bruno Vincenzi (ORCID: https://orcid.org/0000-0001-8222-9025)
- Aviram Nissan (ORCID: https://orcid.org/0000-0003-0701-2293)
- Jason L. Hornick (ORCID: https://orcid.org/0000-0001-6475-8345)
- Emily Z. Keung (ORCID: https://orcid.org/0000-0002-8783-8484)
- Miguel Henriques Abreu
- José Antonio González López
Institutions
- Brigham and Women's Hospital (US)
- University Hospitals Birmingham NHS Foundation Trust (GB)
- The University of Texas MD Anderson Cancer Center (US)
- Harvard University (US)
- University of Ottawa (CA)
- Università Campus Bio-Medico (IT)
- The University of Melbourne (AU)
- University of Washington (US)
- Leeds Teaching Hospitals NHS Trust (GB)
- Sheba Medical Center (IL)
- Peter MacCallum Cancer Centre (AU)
- Hospital de Sant Pau (ES)
- LMU Klinikum (DE)
- Instituto Português de Oncologia Francisco Gentil (PT)
- Dana-Farber Cancer Institute (US)
- Candiolo Cancer Institute (IT)
- Istituti di Ricovero e Cura a Carattere Scientifico (IT)
- Fondazione IRCCS Istituto Nazionale dei Tumori (IT)
- Ludwig-Maximilians-Universität München (DE)
Publication Details
- Journal
- Annals of Surgical Oncology
- Published
- 2025-07-14
- DOI
- https://doi.org/10.1245/s10434-025-17787-8
- Citations
- 1
- Primary Topic
- Tuberous Sclerosis Complex Research
- Type
- article
- Field-Weighted Citation Impact
- 1.16
Funders
- University of Melbourne