Ovarian Fibrosarcoma: 1 Case Report and Review of the Literature

Ovarian fibrosarcoma is an extremely rare malignant tumor, accounting for less than 1% of all ovarian tumors. It is characterized by a proliferation of spindle-shaped cells with high mitotic activity, often posing a diagnostic challenge due to its resemblance to certain benign tumors. Diagnosis is based on histopathological analysis, possibly supplemented by immunohistochemistry. Treatment is essentially surgical, while the role of chemotherapy remains controversial in the absence of consensus. Prognosis depends on histological aggressiveness and stage at diagnosis. This paper summarizes current knowledge of this rare entity and highlights the need for better data collection through multicenter studies.