Autoimmune-associated hemophagocytic syndrome complicated by anti-MDA5 antibody-positive dermatomyositis successfully treated with immunosuppressive therapy: A case report
This case underscores the importance of early recognition of hemophagocytic syndrome in patients with anti-MDA5-positive dermatomyositis. Prompt bone marrow evaluation and aggressive immunosuppressive therapy may lead to favorable long-term outcomes. Further studies are warranted to establish standardized treatment strategies for autoimmune-related hemophagocytic syndrome.
Authors
- Tetsuri Kondo (ORCID: https://orcid.org/0000-0001-5975-1886)
- Makoto Hibino (ORCID: https://orcid.org/0000-0002-1638-5027)
- Takuya Kakutani
- Riko Kamada (ORCID: https://orcid.org/0000-0003-1675-1362)
- Noriyoshi Ishikawa (ORCID: https://orcid.org/0000-0001-5741-0981)
- Kazunari Maeda
- Shigehiro Watanabe
- Hikari Higa
Institutions
- Fujisawa City Hospital (JP)
- Shonan Oiso Hospital (JP)
- Shonan Kamakura General Hospital (JP)
Publication Details
- Journal
- Medicine
- Published
- 2025-07-04
- DOI
- https://doi.org/10.1097/md.0000000000043229
- Primary Topic
- Autoimmune and Inflammatory Disorders Research
- Type
- article
- Field-Weighted Citation Impact
- 0.00