Giant Darier-Ferrand Dermatofibrosarcoma of the Scalp: A Case Report

Dermatofibrosarcoma (DFS) is a slow-growing fibrous tumor of the skin with a very high risk of local recurrence but low metastatic potential. In this work, we report a case of a 43-year-old male patient who was treated in the university hospital of Ibn Sina of Rabat for a giant DFS of the scalp. This entity represents a tumor whose prognosis and risk of progression are mainly linked to the diagnostic delay and the quality of the first excision. Late diagnosis makes excision and reconstruction surgery difficult like in our case. The chances of cure in the case of well-conducted primary surgery are significantly higher than those of salvage surgery. Improving the prognosis requires early and codified multidisciplinary care, hence the importance of raising awareness and informing the general practitioner for early diagnosis and correct referral of these patients to specialist centers.