OHVIRA Syndrome in a 13-Year-Old Girl: A Case Report and Literature Review

OHVIRA (Obstructed Hemivagina and Ipsilateral Renal Anomaly) syndrome, or Herlyn-Werner-Wunderlich syndrome, is a rare malformation of the female reproductive tract combining a didelphic uterus, obstructed hemivagina and homolateral renal agenesis. It usually manifests at puberty as cyclical pelvic pain and severe dysmenorrhea. Diagnosis is based on imaging, in particular MRI, which enables precise evaluation of pelvic structures. Treatment is surgical, based on resection of the obstructive vaginal septum. We report a case of ohvira syndrome in a 13-year-old girl in the maternity ward at the abderrahim Harouchi university hospital in Casablanca.