A Case of Langerhans Cell Histiocytosis That Was Initially Suspected as Congenital Middle Ear Cholesteatoma

Langerhans cell histiocytosis (LCH) is a rare disease characterized by abnormal clonal proliferation of Langerhans cells, which are antigen-presenting cells derived from the bone marrow, along with inflammatory cell infiltration. The disease can present as a solitary lesion or multisystem lesions, reflecting a diverse clinical spectrum. LCH lesions in the head and neck region are relatively common, accounting for approximately 70% of all the cases, and these patients are often evaluated by otolaryngologists.