Juvenile dermatomyositis: a severe and atypical presentation

This is an atypical presentation of JDM, without the typical skin lesions, but with several manifestations of severe vasculopathy, including retinopathy and alveolar haemorrhage. Early diagnosis and a multidisciplinary approach are crucial to improve prognosis.

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Publication Details

Journal
ARP Rheumatology
Published
2025-06-30
DOI
https://doi.org/10.63032/nzhm3565
Primary Topic
Inflammatory Myopathies and Dermatomyositis
Type
article
Field-Weighted Citation Impact
0.00
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article

Juvenile dermatomyositis: a severe and atypical presentation

Maria Eduarda de Souza Andrade, Patrícia Costa‐Reis, A. Marques, Isabel Almeida et al.
ARP Rheumatology
Inflammatory Myopathies and Dermatomyositis
article

Juvenile dermatomyositis: a severe and atypical presentation

Maria Eduarda de Souza Andrade, Patrícia Costa‐Reis, A. Marques, Isabel Almeida, Filipa Oliveira‐Ramos, Miguel Bernardo, Ana Cláudia Fonseca
article en

Abstract

This is an atypical presentation of JDM, without the typical skin lesions, but with several manifestations of severe vasculopathy, including retinopathy and alveolar haemorrhage. Early diagnosis and a multidisciplinary approach are crucial to improve prognosis.

ARP RheumatologyVol. 4(2)
Hospital de Santa Maria (PT)
Openalex Percentile: Top 78%
Inflammatory Myopathies and Dermatomyositis
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Juvenile dermatomyositis: a severe and atypical presentation — Maria Eduarda de Souza Andrade, Patrícia Costa‐Reis, et al. · ARP Rheumatology (2025) | TGRS Research Map | TGRS