Aborted sudden cardiac event in pediatric restrictive cardiomyopathy: When ST changes on ambulatory monitoring matter

Restrictive cardiomyopathy (RCM) is a rare disease in the pediatric population, only accounting for 2-5% of cardiomyopathy diagnoses.1-4 RCM is defined as biventricular failure due to impaired ventricular filling and has no identifiable causes in most pediatric cases.5 Unlike other cardiomyopathies, RCM has no direct beneficial medical therapy forcing providers to list for transplant early if there are any concerning symptoms or diagnostics.5 Of the scant literature describing pediatric RCM, 10-25% of the patients described had sudden cardiac events.