Diagnosis, Treatment, and Management of Common Childhood Vasculitides

Childhood vasculitides, including immunoglobulin A vasculitis, Kawasaki disease, Behçet disease, and polyarteritis nodosa, are inflammatory disorders affecting varying-sized blood vessels. Their pathogenesis involves immune dysregulation, genetic predisposition, and environmental triggers. While treatment varies based on disease severity, immunosuppressive therapy is often required. Preventing complications depends mainly on early identification of the disease and initiating appropriate management. This review aims to guide clinicians in the early diagnosis and multidisciplinary management of childhood vasculitides by addressing their pathogenesis, clinical features, diagnostic approaches, and treatment strategies.

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Publication Details

Journal
The Journal of Pediatric Academy
Published
2025-06-20
DOI
https://doi.org/10.4274/jpea.2025.420
Primary Topic
Vasculitis and related conditions
Type
article
Field-Weighted Citation Impact
0.00
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article

Diagnosis, Treatment, and Management of Common Childhood Vasculitides

Nuray Aktay Ayaz, Atalay Doğru, Büşra Başer Taşkın
The Journal of Pediatric Academy
Vasculitis and related conditions
article

Diagnosis, Treatment, and Management of Common Childhood Vasculitides

Nuray Aktay Ayaz, Atalay Doğru, Büşra Başer Taşkın
article en

Abstract

Childhood vasculitides, including immunoglobulin A vasculitis, Kawasaki disease, Behçet disease, and polyarteritis nodosa, are inflammatory disorders affecting varying-sized blood vessels. Their pathogenesis involves immune dysregulation, genetic predisposition, and environmental triggers. While treatment varies based on disease severity, immunosuppressive therapy is often required. Preventing complications depends mainly on early identification of the disease and initiating appropriate management. This review aims to guide clinicians in the early diagnosis and multidisciplinary management of childhood vasculitides by addressing their pathogenesis, clinical features, diagnostic approaches, and treatment strategies.

The Journal of Pediatric Academy
Istanbul University (TR)
Good health and well-being
Openalex Percentile: Top 76%
Vasculitis and related conditions
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