Simple Renal Cysts in Marfan Syndrome
The prevalence of SRCs was significantly higher in patients with MFS compared to matched controls. SRCs were independently associated with aortic dissection in MFS. Prospective studies are needed to further evaluate whether SRCs could represent a marker of aortic disease severity in patients with MFS.
Authors
- Guillaume Jondeau (ORCID: https://orcid.org/0000-0002-0101-2076)
- Maud Langeois
- Olivier Milleron (ORCID: https://orcid.org/0000-0002-6517-0559)
- Maria Tchitchinadze
- Laurent Gouya (ORCID: https://orcid.org/0000-0002-1326-7025)
- Raphaël Thuillier (ORCID: https://orcid.org/0000-0002-7482-0031)
- Gaspard Suc
- Florence Nicot (ORCID: https://orcid.org/0000-0002-6265-4216)
- Noémie Tence
- Cathérine Boileau (ORCID: https://orcid.org/0000-0002-0371-7539)
- Benjamin Alos (ORCID: https://orcid.org/0000-0002-6434-2873)
- Nicoletta Pasi
- Phalla Ou (ORCID: https://orcid.org/0000-0001-5053-077X)
- Florence Arnoult
- Claire Bouleti
Institutions
- Inserm (FR)
- Délégation Paris 7 (FR)
- Université Fédérale de Toulouse Midi-Pyrénées (FR)
- Université Paris Cité (FR)
- Université de Poitiers (FR)
- Université Sorbonne Paris Nord (FR)
- Assistance Publique – Hôpitaux de Paris (FR)
- Laboratoire de Recherche des Monuments Historiques (FR)
- Laboratoire de Recherche Vasculaire Translationnelle (FR)
- Hôpital Bichat-Claude-Bernard (FR)
- Hôpital Privé Jacques Cartier (FR)
- Centre Hospitalier de Versailles (FR)
Publication Details
- Journal
- JACC Advances
- Published
- 2025-06-17
- DOI
- https://doi.org/10.1016/j.jacadv.2025.101870
- Primary Topic
- Aortic aneurysm repair treatments
- Type
- article
- Field-Weighted Citation Impact
- 0.00
Funders
- Société Française de Cardiologie