Primary Pulmonary Ewing Sarcoma or Askin Tumor (PNET of the Thoracopulmonary Region) - a Rare Clinical Case in our Practice

Primary pulmonary Ewing sarcoma is a rare disease belonging to the Еwing sarcoma tumor family. The origin of these rarely diagnosed primary undifferentiated neoplasms with possible localization in different organs and tissue structures is still unknown. We present a rare clinical case of primary pulmonary extraskeletal Ewing sarcoma in a woman 35 years old. The purpose of this article is to emphasize the difficult histological and differential diagnosis, requiring a wide panel of immunohistochemical markers. Despite the maximum possible radical surgery, given the local biological malignancy of this exceptionally rare tumor with a poor prognosis, we performed postoperative intensity modulated radiotherapy (IMRT).