Exostosis at the inner ear canal

Exostosis of the IAC is a rare finding that may present with disabling symptoms of dizziness, hearing loss, and vestibular dysfunction. Exostosis can often be confused with IAC osteomas. The purpose of this case report is to discuss the presentation of a patient who presented with this finding. Diagnosis can be delayed and confused with other, more common pathologies. Imaging is fundamental in arriving at a correct diagnosis. Treatment of exostosis of the internal auditory canal depends on the severity of symptoms and the extent of cranial nerve compression.