Biliary Atresia With Situs Inversus Abdominalis Managed by Kasai Portoenterostomy: A Case Report From Muhimbili National Hospital, Tanzania

Biliary atresia associated with situs inversus abdominalis is a rare congenital combination that complicates diagnosis and surgical orientation. Early recognition, meticulous preoperative planning, and timely Kasai portoenterostomy can achieve favorable short-term outcomes. Surgeons should consider anatomical variations to optimize operative safety and improve biliary drainage and prognosis.

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Publication Details

Journal
Clinical Case Reports
Published
2026-08-27
DOI
https://doi.org/10.1002/ccr3.73419
Primary Topic
Pediatric Hepatobiliary Diseases and Treatments
Type
article
Field-Weighted Citation Impact
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article

Biliary Atresia With Situs Inversus Abdominalis Managed by Kasai Portoenterostomy: A Case Report From Muhimbili National Hospital, Tanzania

Alfred Chibwae, Ally Mwanga, Tariq Aziz, Georvin Haule et al.
Clinical Case Reports
Pediatric Hepatobiliary Diseases and Treatments
article

Biliary Atresia With Situs Inversus Abdominalis Managed by Kasai Portoenterostomy: A Case Report From Muhimbili National Hospital, Tanzania

Alfred Chibwae, Ally Mwanga, Tariq Aziz, Georvin Haule, Rajabu Bakari, Zaitun Bokhary, Novath Ngowi, Brian Kimanthi
article en

Abstract

Biliary atresia associated with situs inversus abdominalis is a rare congenital combination that complicates diagnosis and surgical orientation. Early recognition, meticulous preoperative planning, and timely Kasai portoenterostomy can achieve favorable short-term outcomes. Surgeons should consider anatomical variations to optimize operative safety and improve biliary drainage and prognosis.

Clinical Case ReportsVol. 14(9)
Muhimbili University of Health and Allied Sciences (TZ), Muhimbili National Hospital (TZ)
Openalex Percentile: Top 100%
Pediatric Hepatobiliary Diseases and Treatments
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