Predictive value of liver enzymes in long-term prognosis of hepatic Wilson disease: results from the Wilson AEEH registry

While transaminases are valuable for monitoring WD, they should be used alongside other biomarkers to better predict disease progression.

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Publication Details

Journal
Orphanet Journal of Rare Diseases
Published
2025-06-07
DOI
https://doi.org/10.1186/s13023-025-03821-1
Citations
2
Primary Topic
Trace Elements in Health
Type
article
Field-Weighted Citation Impact
2.24

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article

Predictive value of liver enzymes in long-term prognosis of hepatic Wilson disease: results from the Wilson AEEH registry

Antonio Olveira, Paula Iruzubieta, Esther Pérez‐Herrán, Carolina Muñoz et al.
2 citations
Orphanet Journal of Rare Diseases
Trace Elements in Health
2.24
article

Predictive value of liver enzymes in long-term prognosis of hepatic Wilson disease: results from the Wilson AEEH registry

Antonio Olveira, Paula Iruzubieta, Esther Pérez‐Herrán, Carolina Muñoz, Judith Gómez Camarero, Ana Arencibia Almeida, Sergio Gil-Rojas, Luis García‐Villarreal, Sara Lorente, Zoe Mariñó, Anna Miralpeix, Mònica Pons, Javier Ampuero, Marta Romero-Gutiérrez, Marina Berenguer, José María Pinazo Bandera, Isabel Carmona Soria, María Luisa González Diéguez, Manuel Hernández‐Guerra, Alba Cachero, Manuel Delgado Blanco, Helena Masnou Ridaura, J.M. Moreno Planas, Diego Burgos Santamaría, Gemma Carrión, Ariadna Bono, María Lázaro Ríos, José Ramón Fernández Ramos, P Castellano
article en
2 citations

Abstract

While transaminases are valuable for monitoring WD, they should be used alongside other biomarkers to better predict disease progression.

Orphanet Journal of Rare DiseasesVol. 20(1)
Universidad de Las Palmas de Gran Canaria (ES), Universitat Autònoma de Barcelona (ES), Hospital Universitario de Canarias (ES), Hospital Universitario La Paz (ES), Bellvitge University Hospital (ES), Hospital Universitari i Politècnic La Fe (ES), Hospital Universitario Nuestra Señora de Candelaria (ES), Hospital Universitario Virgen Macarena (ES), Hospital Virgen de la Luz (ES), Complejo Hospitalario Universitario de Santiago (ES), Marqués de Valdecilla University Hospital (ES), Hospital Universitario 12 De Octubre (ES), Hospital Universitario Miguel Servet (ES), Hospital Clínic de Barcelona (ES), Hospital Universitario de Burgos (ES), Hospital Universitario Central de Asturias (ES), Hospital Clínico Universitario Lozano Blesa (ES), Hospital de Cruces (ES), Complexo Hospitalario Universitario A Coruña (ES), Hospital Universitario Virgen del Rocío (ES), Hospital Universitari Germans Trias i Pujol (ES), Complejo Hospitalario Universitario de Albacete (ES), Hospital Clínico Universitario Virgen de la Victoria (ES), Hospital Universitario Ramón y Cajal (ES), Complejo Hospitalario Universitario de Toledo (ES), Instituto de Investigación Biomédica de Málaga (ES), Hospital Universitario Infanta Leonor (ES), Hospital Universitario de Toledo (ES), University of Castilla-La Mancha (ES)
Asociación Española para el Estudio del Hígado
Good health and well-being
Openalex Percentile: Top 13%
Trace Elements in Health
2.24
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