Notochord-derived lesion presenting with cerebrospinal fluid rhinorrhea: illustrative case

This case highlights the need to consider notochordal lesions in patients with idiopathic CSF rhinorrhea, particularly with clival defects. When CSF leakage with a suspected fistula at the central clivus is encountered, a notochord-derived lesion should be considered, and skull base reconstruction should be performed accordingly. https://thejns.org/doi/10.3171/CASE25157.